Next article Search Articles Instructions for authors  Access Statistics | Citation Manager  
STATE OF THE ART  

 Article Access Statistics
    Viewed550    
    Printed31    
    Emailed0    
    PDF Downloaded56    
    Comments [Add]    

Recommend this journal

Anomalous aortic origin of the pulmonary arteries: Case series and literature review


1 Mediterranean Congenital Heart Center – Bambino Gesù – San Vincenzo Hospital, Taormina, Italy
2 Department of General Surgery, Hospital Santo Tomas, Panamá
3 Department of Clinical Directors, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
4 Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
5 Medical Director, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
6 Emeritus Professor, Royal College of London, London, UK
7 Department of Imaging, Bambino Gesù Children's Hospital IRCCS, Rome, Italy

Correspondence Address:
Dr. Salvatore Agati
Director Congenital Heart Surgery, Mediterranean Congenital Heart Center, Bambino Gesù, Taormina
Italy
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/apc.APC_89_18

Rights and Permissions

Year : 2019  |  Volume : 12  |  Issue : 3  |  Page : 248-253

 

SEARCH
Similar in PUBMED
 Related articles

  Article in PDF (1,229 KB)
Email article
Print Article
Add to My List
Anomalous origin of the pulmonary arteries from the ascending aorta is a rare, but severe clinical entity necessitating a scrupulous evaluation. Either the right or the left pulmonary arteries can arise directly from the ascending aorta while the other pulmonary artery retains its origin from the right ventricular outflow tract. Such a finding can be isolated or can coexist with several congenital heart lesions. Direct intrapericardial aortic origin, however, must be distinguished with origin through a persistently patent arterial duct. In the current era, clinical manifestations usually become evident in the newborn rather than during infancy, as used to be the case. They include respiratory distress or congestive heart failure due to increased pulmonary flow and poor feeding. The rate of survival has now increased due to early diagnosis and prompt surgical repair, should now be expected to be at least 95%. We have treated four neonates with this lesion over the past 7 years, all of whom survived surgical repair. Right ventricular systolic pressure was significantly decreased at follow-up. Our choice of treatment was to translocate the anomalous pulmonary artery in end-to-side fashion to the pulmonary trunk. Our aim in this report is to update an Italian experience in the diagnosis and treatment of anomalous direct origin of one pulmonary artery from the aorta, adding considerations on the lessons learned from our most recent review of the salient literature.






[FULL TEXT] [PDF]*
 

 

 

 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
 Related articles
 
 
 Reader Comments
 Email Alert *
  *
 * Requires registration (Free)
 
 STATE OF THE ART
 




1 Mediterranean Congenital Heart Center – Bambino Gesù – San Vincenzo Hospital, Taormina, Italy
2 Department of General Surgery, Hospital Santo Tomas, Panamá
3 Department of Clinical Directors, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
4 Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
5 Medical Director, Bambino Gesù Children's Hospital IRCCS, Rome, Italy
6 Emeritus Professor, Royal College of London, London, UK
7 Department of Imaging, Bambino Gesù Children's Hospital IRCCS, Rome, Italy

Correspondence Address:
Dr. Salvatore Agati
Director Congenital Heart Surgery, Mediterranean Congenital Heart Center, Bambino Gesù, Taormina
Italy
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/apc.APC_89_18

Rights and Permissions

Anomalous origin of the pulmonary arteries from the ascending aorta is a rare, but severe clinical entity necessitating a scrupulous evaluation. Either the right or the left pulmonary arteries can arise directly from the ascending aorta while the other pulmonary artery retains its origin from the right ventricular outflow tract. Such a finding can be isolated or can coexist with several congenital heart lesions. Direct intrapericardial aortic origin, however, must be distinguished with origin through a persistently patent arterial duct. In the current era, clinical manifestations usually become evident in the newborn rather than during infancy, as used to be the case. They include respiratory distress or congestive heart failure due to increased pulmonary flow and poor feeding. The rate of survival has now increased due to early diagnosis and prompt surgical repair, should now be expected to be at least 95%. We have treated four neonates with this lesion over the past 7 years, all of whom survived surgical repair. Right ventricular systolic pressure was significantly decreased at follow-up. Our choice of treatment was to translocate the anomalous pulmonary artery in end-to-side fashion to the pulmonary trunk. Our aim in this report is to update an Italian experience in the diagnosis and treatment of anomalous direct origin of one pulmonary artery from the aorta, adding considerations on the lessons learned from our most recent review of the salient literature.






[FULL TEXT] [PDF]*


        
Print this article     Email this article