Kyle W Riggs, Nina M Price, Nicholas Szugye, Bryan H Goldstein, David L S Morales
Cincinnati Children's Hospital Medical Center, Heart Institute, Cincinnati, OH, USA
We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During comprehensive Stage-II, the ALCAPA was reimplanted in the neoaorta and measures, including a nontraditional Damus connection/arch reconstruction and classic bilateral Glenn procedures, were taken to avoid compression of the coronary artery. After a successful Fontan procedure, he continues to do well at 5 years old, becoming the first patient reported in the literature to survive all the three stages of single-ventricle palliation.
Kyle W Riggs
Cincinnati Children's Hospital Medical Center, Heart Institute, 3333 Burnet Ave MLC 2003, Cincinnati 45229, OH
Source of Support: None, Conflict of Interest: None
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