Annals of Pediatric Cardiology
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First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond Fontan


 Cincinnati Children's Hospital Medical Center, Heart Institute, Cincinnati, OH, USA

Correspondence Address:
Kyle W Riggs,
Cincinnati Children's Hospital Medical Center, Heart Institute, 3333 Burnet Ave MLC 2003, Cincinnati 45229, OH
USA
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/apc.APC_152_18

We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During comprehensive Stage-II, the ALCAPA was reimplanted in the neoaorta and measures, including a nontraditional Damus connection/arch reconstruction and classic bilateral Glenn procedures, were taken to avoid compression of the coronary artery. After a successful Fontan procedure, he continues to do well at 5 years old, becoming the first patient reported in the literature to survive all the three stages of single-ventricle palliation.


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    -  Riggs KW
    -  Price NM
    -  Szugye N
    -  Goldstein BH
    -  Morales DL
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