Year : 2014  |  Volume : 7  |  Issue : 3  |  Page : 207--209

Hypoplastic left heart syndrome secondary to intrauterine rhabdomyoma necessitating single ventricle palliation


Arshid Mir1, Catherine Minor Ikemba2, Surendranath R Veeram Reddy2 
1 Department of Pediatrics, Division of Cardiology, Oklahoma University Children Hospital, Oklahoma University Health Sciences Center, Oklahoma City, Oklahoma, USA
2 Department of Pediatrics, Division of Cardiology, University of Texas Southwestern Medical Center, Children Medical Center Dallas, Dallas, Texas, USA

Correspondence Address:
Arshid Mir
Department of Pediatrics, Division of Cardiology, Oklahoma University Children Hospital, Oklahoma University Health Sciences Center, 1200 Everett Drive, Suite NP 2350, Oklahoma City, Oklahoma
USA

Rhabdomyoma, a benign hamartomatous tumor of the cardiac embryonic myocyte, is the most common intrauterine cardiac tumor and accounts for 0.12% of prenatal fetal studies. Fetal cardiac rhabdomyomas increase in size during second and early third trimester and spontaneously regress postnatally. The clinical presentation is usually benign, however, compromise of the ventricular outflow tract leading to decreased cardiac output and fetal death have been reported. We present a case of large cardiac rhabdomyoma in a fetus that might have caused complete left ventricular outflow tract obstruction and development of hypoplastic left heart syndrome (HLHS) necessitating postnatal single ventricle palliation therapy. The clinical course and outcomes of prenatally diagnosed cardiac rhabdomyoma are reviewed and theories of the development of hypoplastic left heart syndrome are explored.


How to cite this article:
Mir A, Ikemba CM, Veeram Reddy SR. Hypoplastic left heart syndrome secondary to intrauterine rhabdomyoma necessitating single ventricle palliation.Ann Pediatr Card 2014;7:207-209


How to cite this URL:
Mir A, Ikemba CM, Veeram Reddy SR. Hypoplastic left heart syndrome secondary to intrauterine rhabdomyoma necessitating single ventricle palliation. Ann Pediatr Card [serial online] 2014 [cited 2020 Sep 25 ];7:207-209
Available from: http://www.annalspc.com/article.asp?issn=0974-2069;year=2014;volume=7;issue=3;spage=207;epage=209;aulast=Mir;type=0