Year : 2016  |  Volume : 9  |  Issue : 2  |  Page : 179--182

Creating a Fontan fenestration in a child with dextrocardia and interrupted inferior vena cava


Pradeepkumar Charlagorla, John P Breinholt 
 Department of Pediatrics, Division of Cardiology, Riley Hospital for Children, Indiana University School of Medicine, Indianapolis, Indiana, USA

Correspondence Address:
Pradeepkumar Charlagorla
Riley Hospital for Children, Indiana University School of Medicine, 705 Riley Hospital Drive RR127, Indianapolis - 46202, Indiana
USA

Plastic bronchitis is a rare life-threatening complication of the Fontan operation. Transcatheter Fontan fenestration can ameliorate symptoms by decompressing elevated venous pressures. Transcatheter creation of a fenestration can be technically challenging in cases with complex venous anatomy. We report a case of a 5-year-old boy with heterotaxy, dextrocardia with unbalanced atrioventricular canal (AVC), atrial and visceral situs inversus, left-sided superior vena cava (SVC), and left-sided interrupted inferior vena cava (IVC) with azygos continuation. With few modifications to the equipment, a successful Fontan fenestration with stent implantation was performed via transjugular approach. At 2-year follow-up, his symptoms of plastic bronchitis improved significantly.


How to cite this article:
Charlagorla P, Breinholt JP. Creating a Fontan fenestration in a child with dextrocardia and interrupted inferior vena cava.Ann Pediatr Card 2016;9:179-182


How to cite this URL:
Charlagorla P, Breinholt JP. Creating a Fontan fenestration in a child with dextrocardia and interrupted inferior vena cava. Ann Pediatr Card [serial online] 2016 [cited 2020 May 28 ];9:179-182
Available from: http://www.annalspc.com/article.asp?issn=0974-2069;year=2016;volume=9;issue=2;spage=179;epage=182;aulast=Charlagorla;type=0