Year : 2019  |  Volume : 12  |  Issue : 2  |  Page : 153--155

Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum


Anand Subramanian, AP Bharath, M Jayaranganath 
 Department of Pediatric Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Bengaluru, Karnataka, India

Correspondence Address:
Dr. Anand Subramanian
Department of Pediatric Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Bengaluru - 560 069, Karnataka
India

An unguarded atrioventricular orifice is an extremely rare congenital anomaly characterized by the absence of the atrioventricular valve in varying proportions. While atresia of the mitral or aortic valves are usually described as causes for hypoplastic left heart, our case highlights the role of free atrioventricular valve regurgitation and consequent volume loss of the left heart, giving rise to a small left ventricle. There was an associated double-outlet right ventricle and Type B aortic interruption. While we have attempted to discuss the complex management options in this scenario, the parents decided to withdraw further care.


How to cite this article:
Subramanian A, Bharath A P, Jayaranganath M. Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum.Ann Pediatr Card 2019;12:153-155


How to cite this URL:
Subramanian A, Bharath A P, Jayaranganath M. Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum. Ann Pediatr Card [serial online] 2019 [cited 2019 Jun 17 ];12:153-155
Available from: http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=2;spage=153;epage=155;aulast=Subramanian;type=0