Paolo Ferrero1, Isabelle Piazza1, Nageswara Rao Koneti2, Matteo Ciuffreda1
1 Cardiovascular Department, Division of Cardiology, ASST Papa Giovanni XXIII, Bergamo, Italy
2 Department of Pediatric Cardiology, Rainbow Children Heart Hospitals, Hyderabad, Telangana, India
Total anomalous pulmonary venous drainage (TAPVD) encompasses a wide spectrum of anatomical variants. The infradiaphragmatic type is almost always obstructive owing to the interposition of intrahepatic resistances; since almost invariable, the vertical vein inserts on the portal venous system. On correction of this variant, the vertical vein might not be ligated to avoid postoperative pulmonary hypertension. We hereby describe an unusual case of infradiaphragmatic TAPVD, with a vertical vein connected to ductus venosus. Since vertical vein was not ligated, it realized an unrestrictive pathway between the left atrium and the suprahepatic veins which resulted in persistent chylous peritoneal drainage. The patient successfully underwent catheter occlusion of the vertical vein which led to complete resolution of the clinical picture.
Dr. Paolo Ferrero
ASST Papa Giovanni XXIII, Piazza OMS, 1, 24127 Bergamo
Source of Support: None, Conflict of Interest: None
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