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Transposition of the great arteries with total anomalous pulmonary venous connection in a 1½year-old child: Pulmonary arterial hypertension - An advantage
Rose Okwunu Abah1, Atul Prabhu2, Ashish Katewa2, Balswaroop Sahu2
1 Department of Paediatrics, Benue State University Teaching Hospital, Benue State University, Makurdi, Nigeria 2 Sri Sathya Sai Sanjeevani International Paediatric Cardiac Centre, Raipur, Chhattisgarh, India
Correspondence Address:
Rose Okwunu Abah, Department of Paediatrics, Benue State University Teaching Hospital, Makurdi Nigeria
 Source of Support: None, Conflict of Interest: None DOI: 10.4103/apc.APC_65_20
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Transposition of the great arteries with total anomalous pulmonary venous connection is a rare anomaly with varied management approach depending on the time of presentation; the management of cases which present early is usually by anatomical surgical approach while late presentation is by physiologic approach. This is due to early left ventricular mass regression as a result of the absence of volume and pressure load to the left ventricle (LV). We report a late presentation (at 1½ years of age) that had a successful anatomic surgical correction because the LV was “prepared” by both pressure and volume load from pulmonary arterial hypertension and large ostium secundum atrial septal defect.
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