Year : 2016  |  Volume : 9  |  Issue : 1  |  Page : 49--52

Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent


Osamah Aldoss, Benjamin E Reinking, Abhay Divekar 
 Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Children's Hospital, Iowa City, Iowa, USA

Correspondence Address:
Osamah Aldoss
Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Children«SQ»s Hospital, 200 Hawkins Dr., Iowa City - 52242, Iowa
USA

A 6-year-old male child born with hypoplastic left heart syndrome (HLHS) was palliated with an extracardiac nonfenestrated Fontan procedure (18-mm Gore-Tex tube graft). He developed low-pressure (mean Fontan pressure 10 mmHg) protein-losing enteropathy 6 months after Fontan palliation. After initially responding to medical therapy and transcatheter pulmonary artery stent implantation, he developed medically refractory protein-losing enteropathy. At this time, his transthoracic echocardiogram showed new restriction across his native atrial septum with an 8 mmHg mean gradient. Cardiac catheterization now showed high-pressure (mean Fontan pressure 18-20 mmHg) protein-losing enteropathy and a new 6 mmHg mean gradient across the atrial septum. To avoid cardiopulmonary bypass, he underwent successful transcatheter relief of atrial septal restriction and creation of a fenestration with rapid clinical and biochemical improvement of his protein-losing enteropathy.


How to cite this article:
Aldoss O, Reinking BE, Divekar A. Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent.Ann Pediatr Card 2016;9:49-52


How to cite this URL:
Aldoss O, Reinking BE, Divekar A. Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent. Ann Pediatr Card [serial online] 2016 [cited 2021 May 12 ];9:49-52
Available from: https://www.annalspc.com/article.asp?issn=0974-2069;year=2016;volume=9;issue=1;spage=49;epage=52;aulast=Aldoss;type=0